Juvenile Nasopharyngeal Angioblastoma is a benign tumor of the nasal cavities occurring almost entirely in males anywhere from 14 to 18 years old. The article goes on further more to say that if a female is diagnosed that this particular diagnosis should be questioned and undergo chromosomal studies…wow I know, right? It is most commonly found in the back of the nose and upper throat. This noncancerous growth is not common and occurs in about 1 in 60,000 nose and throat patients. Instead of invading surrounding tissue, it adds pressure which therefore distorts and displaces. This causes necrosis of tissue by pressure. Intracranial extension happen in about 10 to 20% of cases. How the tumor occurs no one knows for sure, but scientists predict it derives from sex-steroid tissue located in the nasal cartilage.
Symptons include bloody snot from the nose, rhinorrhea (more commonly called a runny nose), loss of hearing, eye pain, and double vision.
Treatments vary for this disease. To reduce the size of the tumor, doctors can use hormonal treatments, chemotherapy, or external beam irradiation. Surgery greatly depends on the location and the size of the tumor. CTs and MRIs help map out the possibility of this option, as well as help diagnose this disease.
Below is a junvile boy with angiofibroma. Notice the bulge of his eyes and middle of his face due to the pressure of the tumor.
http://eyepathologist.com/images/KL18434.jpg
This is a contrast ehanced axial MR image of the tumorright behind and into the nasal cavity.
http://www.radpod.org/wp-content/uploads/2007/07/juvenile_angiofibroma_gd_ax.jpg
No comments:
Post a Comment